Protein misfolding and mislocalization are common to both familial and sporadic forms of amyotrophic lateral sclerosis (ALS). Maintaining proteostasis
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[title] => Reversal of cognitive deficits in FUSR521G amyotrophic lateral sclerosis mice by
[paragraph] => Reversal of cognitive deficits in FUSR521G amyotrophic lateral sclerosis mice by arimoclomol and a class I histone deacetylase inhibitor independent of heat shock protein induction
[content] => Authors
Mari Carmen Pelaez, Frédéric Fiore, Nancy Larochelle, Afrooz Dabbaghizadeh, Mario Fernandez Comaduran, Danielle Arbour, Sandra Minotti, Laetitia Marcadet, Martine Semaan, Richard Robitaille, Josephine N. Nalbantoglu, Chantelle F. Sephton, Heather D. Durham
Lab
Journal
Neurotherapeutics
Abstract
Protein misfolding and mislocalization are common to both familial and sporadic forms of amyotrophic lateral sclerosis (ALS). Maintaining proteostasis
Keywords/Topics
Amyotrophic; lateral sclerosis;Heat shock ;proteins;FUSArimoclomol;Histone deacetylase inhibitor;Frontotemporal dementia
BIOSEB Instruments Used:
Grip strength test (BIO-GS4)
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[description_short] => Une méthode simple pour quantifier objectivement la force musculaire des rats et souris et l'effet de drogues, toxines, maladies musculaires (ex: myopathie) et neurodégénératives. Cette mesure de force est souvent employée en association avec le test de coordination motrice ROTAROD: un sujet présentant une coordination normale montrera des résultats médiocres en cas de faible force musculaire. Un must pour vos recherches sur l'activité, la coordination et le contrôle musculaire: particulièrement utile pour vos études sur les maladies de Parkinson et Huntington.
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